Rare case of megacystis-microcolon syndrome in newborn

Megacystis microcolon intestinal hypoperistaltis syndrore (MMIHS) is rare cause of intestinal obstruction in neonates. It poses a diagnostic and therapeutic challenge to the surgeon. An inflammatory process has been suggested involving the GI tract and the bladder. The key to diagnosis is enlarged bladder and myopathy demonstrated on intestinal histopathology. The long term prognosis is bad. We report this rarity with a review of various aspects of the disease.