Structure of congenital nephropathies in children of the Republic of Mordovia

The article describes the results of a retrospective analysis of 30 patient histories of children with congenital nephropathies aged from 2 days to 17 y/o. The majority of cases of congenital nephropathies in children of the Republic of Mordovia for the period of 2015-2022 were diagnosed during examination for other pathologies and upon referral (60%). The structure of congenital nephropathies in children is dominated by anomalies of kidney differentiation (50%) represented mainly by cystic dysplasia and tubulopathies (20%). Congenital glomerulopathies and tubulopathies were diagnosed in the first three years of life, while an anomaly in the formation of renal tissue with parenchyma deficiency (normonephronic hypoplasia) and more than half of the cases (64.3%) of cystic dysplasia were identified after 4 years of age.