Cystic kidney dysplasia in infants

Cystic kidney dysplasia (CKD) in infants is a rare congenital pathology, associated with connective tissue dysplasia. Three autopsy cases of CKD reveals disturbance proportions of connective, fat, chondroid tissue with dominance cells and fibers of connective tissue. Kidney cysts formation with CKD, under our opinion, is secondary process due to compression few kidney tubules by undeveloped mesenchymal tissue.